Butterfly-shaped Pattern Dystrophy : Findings of Retinal Imaging

Houda Bezza *

Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.

Amine Mounsif

Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.

Zineb Algouti

Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.

Youssef Bennouk

Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.

Houssaine Ait Lhaj

Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.

Mohamed Kriet

Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.

Fouad Elasri

Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.

*Author to whom correspondence should be addressed.


Abstract

Butterfly shaped pattern dystophy (BPD) is a inherited macular disease which is characterized by the accumulation of pigment/lipofuscin in the retinal pigment epithelium, it might be misdiagnosed as age-related macular degeneration (AMD). Retinal imaging is a useful tool for the differential diagnosis of pattern dystrophy. In this report, we describe a 64 year old man presented metamorphopsia and reduced visual acuity in both eyes. Fundus examination showed an area of depigmentation delimited resembling a butterfly. The OCT revealed a subfoveal hyperreflective deposit above the retinal pigment epithelium (RPE) while fundus autofluorescence (FAF) shows hypoautofluorescent areas outlined by a lipofuscin deposits as hyperautofluorescent Finally, fluoroscein angiography (FFA) revealed early macular hyperfluorescence. 

Keywords: Butterfly shaped pattern dystophy, macular dytrophy, retinal imaging, AMD


How to Cite

Bezza , H., Mounsif , A., Algouti, Z., Bennouk , Y., Lhaj , H. A., Kriet , M., & Elasri , F. (2024). Butterfly-shaped Pattern Dystrophy : Findings of Retinal Imaging. Ophthalmology Research: An International Journal, 19(1), 26–30. https://doi.org/10.9734/or/2024/v19i1411

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