Butterfly-shaped Pattern Dystrophy : Findings of Retinal Imaging
Houda Bezza *
Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.
Amine Mounsif
Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.
Zineb Algouti
Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.
Youssef Bennouk
Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.
Houssaine Ait Lhaj
Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.
Mohamed Kriet
Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.
Fouad Elasri
Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.
*Author to whom correspondence should be addressed.
Abstract
Butterfly shaped pattern dystophy (BPD) is a inherited macular disease which is characterized by the accumulation of pigment/lipofuscin in the retinal pigment epithelium, it might be misdiagnosed as age-related macular degeneration (AMD). Retinal imaging is a useful tool for the differential diagnosis of pattern dystrophy. In this report, we describe a 64 year old man presented metamorphopsia and reduced visual acuity in both eyes. Fundus examination showed an area of depigmentation delimited resembling a butterfly. The OCT revealed a subfoveal hyperreflective deposit above the retinal pigment epithelium (RPE) while fundus autofluorescence (FAF) shows hypoautofluorescent areas outlined by a lipofuscin deposits as hyperautofluorescent Finally, fluoroscein angiography (FFA) revealed early macular hyperfluorescence.
Keywords: Butterfly shaped pattern dystophy, macular dytrophy, retinal imaging, AMD