A Case Report on IRVAN Syndrome
Houda Bezza *
Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.
Asma El Adrari
Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.
Oumayma El Mansouri
Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.
Kawtar Zaoui
Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.
Lhoussaine Ait Lhaj
Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.
Mohamed Kriet
Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.
Fouad Elasri
Ophthalmology Department, Avicenna Military Hospital of Marrakech, Morocco.
*Author to whom correspondence should be addressed.
Abstract
Idiopathic retinal vasculitis, arteriolar macroaneurysms, and neuroretinitis (IRVAN) is a rare condition predominantly affecting young, healthy females without systemic disease. We present the case of a 35-year-old female who presented with a 3-month history of decreased visual acuity without associated symptoms. Ophthalmological examination revealed reduced visual acuity in both eyes, papillary oedema, stellate macular oedema, and haemorrhages bilaterally. Retinal imaging confirmed IRVAN syndrome. Treatment included pan-retinal photocoagulation (PRP) and intravitreal bevacizumab injections, resulting in macular oedema regression.
Keywords: Vasculitis, arteriolar macroaneurysms, neuroretinitis, anti VEGF, PRP