Management of a Bilateral Ectopia Lentis in a Patient with Marfan Syndrome: A Case Report

EL Filali El Mehdi *

Department of Ophthalmology, Cadi Ayyad University, MED VI University Hospital, Avicenne Military Hospital, Marrakech, Morocco.

Zineb Algouti

Department of Ophthalmology, Cadi Ayyad University, MED VI University Hospital, Avicenne Military Hospital, Marrakech, Morocco.

Farah Benelkadri

Department of Ophthalmology, Cadi Ayyad University, MED VI University Hospital, Avicenne Military Hospital, Marrakech, Morocco.

Houssaine Aitlhaj

Department of Ophthalmology, Cadi Ayyad University, MED VI University Hospital, Avicenne Military Hospital, Marrakech, Morocco.

Mohamed Kriet

Department of Ophthalmology, Cadi Ayyad University, MED VI University Hospital, Avicenne Military Hospital, Marrakech, Morocco.

Fouad El Asri

Department of Ophthalmology, Cadi Ayyad University, MED VI University Hospital, Avicenne Military Hospital, Marrakech, Morocco.

*Author to whom correspondence should be addressed.


Abstract

AIMS: to highlight the management procedure of a bilateral subluxated lens in a patient with marfan syndrome.

Case Report: We report a case of a 51-year-old woman, with a family history of Marfan syndrome; who presented for a bilateral subluxated lens, iridodonesis and bilateral macular degeneration. Given the family history, the general physical features and the ocular findings, diagnostic of Marfan syndrome was established. The management of the ectopic lentis was very challenging. An intracapsular lens extraction with posterior chamber intraocular lens fixed to the sclera was performed and the patient regained 2/10 visual acuity on the right eye and remained at counting fingers in the left.

Conclusion: Marfan syndrome is a rare condition, with various ocular manifestations. The only guarantee for a better visual outcome is a well-designed therapeutic approach.

Keywords: Bilateral ectopia lentis, marfan syndrome, tissue disorder


How to Cite

Mehdi , E. F. E., Algouti , Z., Benelkadri , F., Aitlhaj , H., Kriet , M., & Asri , F. E. (2024). Management of a Bilateral Ectopia Lentis in a Patient with Marfan Syndrome: A Case Report. Ophthalmology Research: An International Journal, 19(3), 37–41. https://doi.org/10.9734/or/2024/v19i3424

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